Complete Right Bundle Branch Block in Arrhythmogenic Cardiomyopathy: Similarities to Brugada Syndrome

Peters Stefan
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Abstract

Background: In arrhythmogenic cardiomyopathy complete right bundle branch block do appear. In rare cases complete right bundle branch block with Brugada-like presentation. Method: In 24 patients with typical arrhythmogenic cardiomyopathy ECG showed complete right bundle branch block. In 17 cases atypical RBBB with low voltage were present, in 7 cases typical rSR’ RBBB occurred. Results: Brugada-like ECG could be excluded in 6 cases of typical complete rSR’ right bundle branch block, only in one case Brugada ECG with coved-type ST segment elevation, sharp upstroke and symmetrical T-wave inversion was present. Conclusion: In typical arrhythmogenic cardiomyopathy atypical low voltage and typical rSR’ right bundle branch block appear. Only in one case with typical arrhythmogenic cardiomyopathy the ECG resembles classical Brugada ECG. In right bundle branch block both-arrhythmogenic cardiomyopathy and Brugada-like syndrome-could be presented as an overlap syndrome.
致心律失常心肌病的完全右束支阻滞:与Brugada综合征相似
背景:致心律失常性心肌病确实出现完全性右束支阻滞。在极少数情况下,完整的右束分支阻滞伴brugada样表现。方法:对24例典型致心律失常心肌病患者的心电图表现为完全性右束支阻滞。17例出现低电压非典型RBBB, 7例出现典型rSR RBBB。结果:6例典型完全性rSR右束支传导阻滞均可排除Brugada样心电图,仅1例Brugada心电图表现为cod型ST段抬高、急剧上冲程、对称t波反转。结论:典型的心律失常性心肌病出现不典型的低电压和典型的rSR右束支传导阻滞。只有一例典型的心律失常性心肌病的心电图与经典的Brugada心电图相似。在右束分支阻滞中,致心律失常心肌病和brugada样综合征均可表现为重叠综合征。
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