Hemophagocytic lymphohistiocytosis in children- A case series

Sujatha Ramabhatta, Pushpalatha Kariyappa, M. Manjunath, Manjesh Kurupalya Annayappa
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Abstract

Hemophagocytic Lymphohistiocytosis (HLH) is a rare disorder in children characterised by immune dysregulation and is a potentially life threatening condition. Early initiation of therapy is found to reduce mortality in HLH. A high index of suspicion in children presenting with prolonged fever is needed for early diagnosis of HLH.
儿童嗜血球性淋巴组织细胞增多症-一个病例系列
噬血细胞性淋巴组织细胞增多症(HLH)是一种罕见的儿童疾病,其特征是免疫失调,是一种潜在的危及生命的疾病。发现早期开始治疗可降低HLH的死亡率。早期诊断HLH需要对表现为长时间发热的儿童进行高度怀疑。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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